Hyper-IgM syndrome is an immunodeficient state characterized by a normal to elevated serum concentration of IgM with low or absent IgG, IgA and IgE. A rare form of hyper-IgM syndrome, X-linked, is ... Medical Xpress: Immune System Diseases: News and Research on Hyper-IgM Immunodeficiency Syndrome, Type 1 Immune System Diseases: News and Research on Hyper-IgM Immunodeficiency Syndrome, Type 1 The two-day drive at the University of Minnesota Rochester focused on finding a donor for Ari Chambers-Baltz, a 1-year-old with hyper IgM syndrome.

Understanding the Context

Retired Mayo Clinic nurse Sharon Chambers and her ... Hyper-IgM syndromes are a group of genetic disorders that make it hard to fight off infections. People with hyper-IgM make very few antibodies, causing them to get sick frequently. Hyper IgM syndrome is a group of rare primary immune deficiency disorders characterized by low or absent levels of serum IgG, IgA, IgE and normal or increased levels of serum IgM.

Key Insights

Hyper-IgM syndrome includes several genetically determined diseases [2,3] but may also be secondary to congenital rubella syndrome [4], use of phenytoin, T cell leukemia, or lymphomas [1]. Hyper IgM syndromes are caused by very rare, one-in-a-million, and potentially life-threatening genetic mutations that severely compromise the immune system and resulting in the individual’s inability to produce antibodies. Hyper-IgM (HIgM) syndromes are extremely rare, inherited primary immunodeficiency (PI) diseases characterized by decreased blood levels of immunoglobulin G (IgG) and normal or elevated levels of immunoglobulin M (IgM). Hyper-IgM syndrome is characterized by normal or high levels of immunoglobulin M (IgM) and decreased levels or absence of other immunoglobulins. As a result, people are more susceptible to bacterial infections.

Final Thoughts

Children with hyper-IgM syndrome have frequent sinus and lung infections. At present, there is a lack of detailed understanding and research on the pathogenesis and treatment of Hyperimmunoglobulin M syndrome (HIGM), Hyperimmunoglobulin E syndrome (HIES), and hyperimmunoglobulin D syndrome (HIDS), and few studies have ... Hyper-IgM Syndrome - Etiology, pathophysiology, symptoms, signs, diagnosis & prognosis from the MSD Manuals - Medical Professional Version. What is Hyper IgM syndrome? Primary immunodeficiency where B cells cannot class-switch, leading to normal or elevated IgM but very low IgG, IgA, IgE levels.